Abstract

Dr. L. Berrada*, H. Rhouda, M. Sahli, A. Sefiani and Y. Kriouile

ABSTRACT

Myositis or Fibroplasia Ossificans Progressiva (MOP or FOP) or Munchmeyer’s disease is a rare genetic disease. Its diagnosis is easy at an advanced stage where standard radiography shows a true ectopic skeleton associated with bilateral malformations of the feet and hands. Its evolution is fatal with the risk of rootedness, petrification and death by restrictive respiratory failure. We report a case of FOP diagnosed in a 9-year-old child. The genetic study confirmed the diagnosis. The aim of this article is to recall the circumstances of discovery, the radiological diagnosis with the importance of the association of characteristic congenital malformations and finally to highlight the difficulties of management and treatment.